Managment of a Patient with a Diagnosis of Wilkie Syndrome

Abstract

Introduction: Wilkie syndrome is a rare cause for upper intestinal obstruction, due to a compression of the duodenum between the abdominal aorta and the superior mesenteric artery, of difficult preoperative diagnosis. Barium study and arteriography are the gold-standard diagnostics. Conservative management has been preferred in individuals with short time of evolution. However, those with chronic disease usually require correction by surgical intervention.

Objective: To present the management of a patient diagnosed with Wilkie syndrome.

Case report: A 57-year-old male patient with emetic syndrome and weight loss of more than three months of evolution. Gastroduodenoscopy showed dilatation of the second duodenal portion due to probable extrinsic compression, while the contrast series revealed stop at the duodenojejunal junction. A transmesocolic latero-lateral duodenojejunostomy was performed, without neighboring drainage and with favorable evolution.

Conclusions: A high index of suspicion is required for an accurate diagnosis of this entity. Duodenojejunostomy is the surgical procedure that offers the best outcomes.